Ioannidis Orestis, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Symeonidis Savvas, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Aggeliki Koltsida, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Papadopoulou Stauroula, Department of Pathology, General Hospital of Thessaloniki “G. Papanikolaou”, Thessaloniki, Greece
Malliora Anastasia, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Christidis Panagiotis, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Ouzounidis Nikolaos, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Efstathios Kotidis, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Pramateftakis Manousos George, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Mantzoros Ioannis, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Angelopoulos Stamatios, Department of Surgery, School of Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece
Introduction: Littoral cell angioma (LCA) is a new subtype of vascular tumor, which has been reported infrequently worldwide. It is associated with visceral malignancies and other immunologic conditions. Clinical case: We present a case of a 70-yearold Caucasian male with a 6-year history of myelodysplastic syndrome, which was investigated for splenomegaly and pancytopenia. Radiological and histopathological examinations revealed an LCA and an open splenectomy were performed. The patient had an uneventful post-operative recovery. Conclusion: LCA is a rare tumor, with atypical presentation often associated with other malignancies or immunologic conditions. Diagnosis is challenging, and so far, splenectomy is the gold standard treatment.
Keywords: Littoral cell angioma. Vascular tumor. Myelodysplastic syndrome. Spleen tumor. Case report.